PROBLEM TO BE SOLVED: To provide an agent for preventing or improving lysosomal storage disease that contains low-molecular-weight compounds, which can be produced relatively conveniently and inexpensively, as an active ingredient.SOLUTION: An agent for preventing or improving lysosomal storage disease contains compounds represented by formula (I0), formula (II) and the like, and at least one compound selected from pharmaceutically acceptable salts thereof when R3 is OH.SELECTED DRAWING: NoneCOPYRIGHT: (C)2018,JPO&INPIT【課題】比較的簡便かつ安価に製造することができる低分子化合物を有効成分とする、ライソゾーム病の予防又は改善剤の提供。【解決手段】式(I0)、式(II)などで表される化合物、並びに、R3がOHのときそれらの医薬的に許容される塩から選択される1種以上の化合物を含む、ライソゾーム病の予防又は改善剤。【選択図】なし
