These compounds are useful for treating Disorders associated with Molybdenum cofactor deficiency. Pharmaceutical compositions and intermediaries.Claim 1, a process for preparing a compound of the formula (1) or a pharmaceutically acceptable salts thereof, wherein the process comprises: (a) reacting a compound of formula (2) with a compound of the formula (3) to produce a compound of the formula (4), where: Each R1 is independentlyH or a protecting Group； (b) protect selectively The Compound of the formula (4) to prepare a compound of the formula (5)； (c) phosphorylate The Compound of the formula (5) to prepare a compound of the formula (6)； (d) oxidize The Compound of the formula (6) to prepare Compound L Formula (7)； and (e) check out the compound of the formula (7) to prepare the compound of the formula(1).Claim 38: a process for preparing a compound of the formula (8) or one of its pharmaceutically acceptable Salt form, where the process comprises: (a) reacting a compound of formula (2) with a compound of the formula (3) to produce a compound of the formula (4), Where: Each R1 is independentlyH or a protecting Group； (b) protect selectively The Compound of the formula (4) to prepare a compound of the formula (5)； (c) phosphorylate The Compound of the formula (5) to prepare a compound of the formula (6)； (d) oxidize The Compound of the formula (6)) to prepare a compound of Formula (9)； and (e) check out the compound of the formula (9) to prepare the compound of the formula(8).Estos compuestos son de utilidad para tratar trastornos asociados con deficiencia de cofactor de molibdeno. Composiciones farmacéuticas e intermediarios.Reivindicación 1: Un proceso para preparar un compuesto de la fórmula (1) o una de sus sales farmacéuticamente aceptables, donde el proceso comprende: (a) hacer reaccionar un compuesto de la fórmula (2) con un compuesto de la fórmula (3) para producir un compuesto de la fórmula (4), en donde: cada R1 es, de modo independiente, H o un grupo pr
