Data from: The magnitude of ivacaftor effects on fluid secretion via R117H-CFTR channels: human in vivo measurements

负责人：

关键词：

R117H-7T;F508del;sweat gland;optical imaging;beta-adrenergic agonists;CFTR channel;cystic fibrosis transmembrane conductance regulator;cystic fibrosis;sweat chloride;ivacaftor;isoproterenol;methacholine

DOI：

doi:10.5061/dryad.8225n

摘要：

intradermally to stimulate CFTR-dependent ‘C-sweat’ and methacholine to stimulate ‘M-sweat’, which persists in CF subjects. We focused on an R117H-7T/F508del