The present invention relates to the use of 4-methyl-2-oxo-2H-1-benzopyran-7-yl-5-thio-β-D-xylopyranoside in the treatment of a mucopolysaccharidosis such as Maroteaux-Lamy syndrome.La présente invention concerne lutilisation du 4-méthyl-2-oxo-2H-l-benzopyran-7- yl-5-thio-β-D-xylopyranoside dans le traitement dune mucopolysaccharidose telle que la maladie de Maroteaux-Lamy.