1. A method of treating amyotrophic lateral sclerosis (ALS) in patients, comprising: administering to the patient an effective amount of substantially chiral pure (6R) -2-amino-4,5,6,7-tetrahydro-6- (propylamino) benzothiazole or a pharmaceutically acceptable thereof salt. 2. The method according to claim 1, in which the treatment includes slowing the progression of amyotrophic lateral sclerosis (ALS), reducing the intensity of symptoms associated with amyotrophic lateral sclerosis (ALS), reducing the incidence of symptoms associated with amyotrophic lateral sclerosis (ALS), reducing body weight loss associated with amyotrophic lateral sclerosis (ALS), reversal of weight loss associated with amyotrophic lateral sclerosis (ALS), delayed mortality and their combination. 3. The method of claim 2, wherein the symptoms associated with amyotrophic lateral sclerosis (ALS) are selected from the group consisting of fine motor function, major motor function, bulbar function, respiratory function, and combinations thereof. The method according to claim 2, in which the symptoms associated with amyotrophic lateral sclerosis (ALS) are selected from the group consisting of walking, speaking, eating, swallowing, writing, climbing stairs, the ability to chop food, turning in bed, salivating, dressing, maintaining hygiene, breathing, dyspnea, orthopnea, respiratory failure, and combinations thereof. 5. The method of claim 1, wherein the effective amount is from about 50 mg to about 300 mg per day. The method of claim 1, wherein the effective amount is from about 150 mg to about 300 mg per day. The method of claim 1, wherein the effective amount is about 300 mg or more per day. Method according1. Способ лечения бокового амиотрофического склероза (БАС) у пациентов, включающий:введение пациенту эффективного количества практически хирально чистого (6R)-2-амино-4,5,6,7-тетрагидро-6-(пропиламино)бензотиазола или его фармацевтически приемлемой соли.2. Способ по п.1, в котором лечение включа
