Sanofi;Universite Pierre et Marie Curie (Paris 6);Centre National De La Recherche Scientifique (C.N.R.S.);Institut National De La Sante Et De La Recherche Medicale (Inserm)
The present invention concerns a neuroglobin agonist for use in the treatment or prevention of a mitochondrial disease associated with respiratory chain complex I (RCCI) deficiency and/or respiratory chain complex III (RCCIII) deficiency.